{"id":12240,"date":"2021-03-19T18:05:21","date_gmt":"2021-03-19T18:05:21","guid":{"rendered":"https:\/\/clone.arsacs.com\/?page_id=12240"},"modified":"2026-08-28T14:28:13","modified_gmt":"2026-08-28T18:28:13","slug":"cest-quoi-larsacs","status":"publish","type":"page","link":"https:\/\/arsacs.com\/fr\/what-is-arsacs\/","title":{"rendered":"C\u2019est quoi l\u2019ARSACS?"},"content":{"rendered":"<div class=\"et_pb_section_0 et_pb_section et_section_regular et_block_section\">\r\n\r\n<div class=\"et_pb_row_0 et_pb_row et_block_row\">\r\n\r\n<div class=\"et_pb_column_0 et_pb_column et_pb_column_1_2 et_block_column et_pb_css_mix_blend_mode_passthrough\">\r\n\r\n<div class=\"et_pb_text_0 et_pb_text et_pb_bg_layout_light et_pb_module et_block_module\"><div class=\"et_pb_text_inner\"><p>L\u2019ataxie spastique autosomique r\u00e9cessive de Charlevoix-Saguenay (ARSACS) est une maladie neurologique h\u00e9r\u00e9ditaire rare qui se manifeste g\u00e9n\u00e9ralement d\u00e8s la petite enfance. Les sympt\u00f4mes apparaissent g\u00e9n\u00e9ralement entre 2 et 5 ans ; ils affectent la motricit\u00e9 et s\u2019aggravent progressivement tout au long de l\u2019adolescence et de l\u2019\u00e2ge adulte, entra\u00eenant souvent une raideur accrue, des difficult\u00e9s \u00e0 marcher et, \u00e0 terme, le recours \u00e0 un fauteuil roulant. Cette affection touche la moelle \u00e9pini\u00e8re et les nerfs p\u00e9riph\u00e9riques. Tirant son nom des r\u00e9gions de Charlevoix et du Saguenay, au Qu\u00e9bec, o\u00f9 elle a \u00e9t\u00e9 identifi\u00e9e pour la premi\u00e8re fois, l\u2019ARSACS est aujourd\u2019hui pr\u00e9sente dans le monde entier et constitue la deuxi\u00e8me ataxie r\u00e9cessive la plus courante apr\u00e8s l\u2019ataxie de Friedreich. <a href=\"https:\/\/arsacs.com\/wp-content\/uploads\/2024\/04\/ATAXIE-MASTER-169-11-25-2013.mov\" target=\"_blank\" rel=\"noopener\">Pr\u00e9sentation vid\u00e9o du Dr. Bernard Brais sur ARSACS.<\/a> \u00a0 Disponible en fran\u00e7ais uniquement.<\/p>\n<\/div><\/div><\/div>\r\n\r\n<div class=\"et_pb_column_1 et_pb_column et_pb_column_1_2 et-last-child et_block_column et_pb_css_mix_blend_mode_passthrough\">\r\n\r\n<div class=\"et_pb_image_0 et_pb_image et_pb_module et_block_module\"><span class=\"et_pb_image_wrap\"><img loading=\"lazy\" decoding=\"async\" src=\"https:\/\/arsacs.com\/wp-content\/uploads\/2021\/07\/About-ARSACS.jpg\" width=\"1200\" height=\"797\" srcset=\"https:\/\/arsacs.com\/wp-content\/uploads\/2021\/07\/About-ARSACS.jpg 1200w, https:\/\/arsacs.com\/wp-content\/uploads\/2021\/07\/About-ARSACS-980x651.jpg 980w, https:\/\/arsacs.com\/wp-content\/uploads\/2021\/07\/About-ARSACS-480x319.jpg 480w\" sizes=\"(min-width: 0px) and (max-width: 480px) 480px, (min-width: 481px) and (max-width: 980px) 980px, (min-width: 981px) 1200px, 100vw\" class=\"wp-image-14622\" title=\"\u00c0 propos d&#039;ARSACS\" \/><\/span><\/div><\/div><\/div><\/div>\r\n\r\n<div class=\"et_pb_section_1 et_pb_section et_section_regular et_block_section et_animated section_has_divider et_pb_bottom_divider\">\r\n\r\n<div class=\"et_pb_row_1 et_pb_row et_pb_equal_columns et_block_row\">\r\n\r\n<div class=\"et_pb_column_2 et_pb_column et_pb_column_3_5 et_block_column et_pb_css_mix_blend_mode_passthrough\">\r\n\r\n<div class=\"et_pb_divider_0 et_pb_divider_hidden et_pb_space et_pb_divider_position_top et_pb_module\"><div class=\"et_pb_divider_internal\"><\/div><\/div><\/div>\r\n\r\n<div class=\"et_pb_column_3 et_pb_column et_pb_column_2_5 et-last-child et_block_column et_pb_css_mix_blend_mode_passthrough\">\r\n\r\n<div class=\"et_pb_text_1 et_pb_text et_pb_bg_layout_light et_pb_module et_block_module\"><div class=\"et_pb_text_inner\"><h6>La recherche au service de la gu\u00e9rison<\/h6>\n<h2>Il y a de l'espoir<\/h2>\n<p>La mission de la Fondation est de d\u00e9couvrir et de d\u00e9velopper un traitement pour l\u2019ataxie spastique r\u00e9cessive autosomique de Charlevoix-Saguenay (ARSACS).<\/p>\n<p>Des progr\u00e8s ont \u00e9t\u00e9 r\u00e9alis\u00e9s au fil des ans dans l\u2019identification de la source de la maladie. Votre appui est crucial pour continuer \u00e0 financer des projets \u00e0 fort potentiel ainsi que des essais cliniques.<\/p>\n<\/div><\/div>\r\n\r\n<div class=\"et_pb_module et_pb_button_module_wrapper et_pb_button_0_wrapper preset--module--divi-button--default_wrapper\"><a class=\"et_pb_button_0 et_pb_button et_pb_bg_layout_dark et_pb_module et_block_module preset--module--divi-button--default\" href=\"https:\/\/arsacs.com\/fr\/donate\/\">Faire un don<\/a><\/div><\/div><\/div><div class=\"et_pb_bottom_inside_divider et-no-transition\"><\/div><\/div>\r\n\r\n<div class=\"et_pb_section_2 et_pb_section et_section_regular et_flex_section\">\r\n\r\n<div class=\"et_pb_row_2 et_pb_row et_flex_row gq_r_fixed_buttons\">\r\n\r\n<div class=\"et_pb_column_4 et_pb_column et_flex_column et_pb_css_mix_blend_mode_passthrough et_clickable et_flex_column_8_24 et_flex_column_8_24_tablet et_flex_column_24_24_phone\">\r\n\r\n<div class=\"et_pb_image_1 et_pb_image et_pb_module et_flex_module\"><span class=\"et_pb_image_wrap\"><img loading=\"lazy\" decoding=\"async\" src=\"https:\/\/arsacs.com\/wp-content\/uploads\/2026\/06\/persons-with-ARSACS.jpg\" title=\"les personnes atteintes du syndrome d&#039;Arsacs\" width=\"1920\" height=\"1280\" srcset=\"https:\/\/arsacs.com\/wp-content\/uploads\/2026\/06\/persons-with-ARSACS.jpg 1920w, https:\/\/arsacs.com\/wp-content\/uploads\/2026\/06\/persons-with-ARSACS-1280x853.jpg 1280w, https:\/\/arsacs.com\/wp-content\/uploads\/2026\/06\/persons-with-ARSACS-980x653.jpg 980w, https:\/\/arsacs.com\/wp-content\/uploads\/2026\/06\/persons-with-ARSACS-480x320.jpg 480w\" sizes=\"(min-width: 0px) and (max-width: 480px) 480px, (min-width: 481px) and (max-width: 980px) 980px, (min-width: 981px) and (max-width: 1280px) 1280px, (min-width: 1281px) 1920px, 100vw\" class=\"wp-image-26507\" \/><\/span><\/div>\r\n\r\n<div class=\"et_pb_icon_0 et_pb_icon et_pb_module et_flex_module\"><span class=\"et_pb_icon_wrap\"><span class=\"et-pb-icon\">\ue08a<\/span><\/span><\/div>\r\n\r\n<div class=\"et_pb_text_2 et_pb_text et_pb_bg_layout_light et_pb_module et_flex_module\"><div class=\"et_pb_text_inner\"><h3>Personnes atteintes de l\u2019ARSACS<\/h3>\n<p>Vous avez re\u00e7u un diagnostic d\u2019ARSACS, vous n\u2019\u00eates pas seul. Des personnes atteintes de l\u2019ARSACS se retrouvent partout dans le monde.  Il y a de l\u2019espoir, car la recherche gu\u00e9rit.<\/p>\n<\/div><\/div>\r\n\r\n<div class=\"et_pb_module et_pb_button_module_wrapper et_pb_button_1_wrapper preset--module--divi-button--default_wrapper\"><a class=\"et_pb_button_1 et_pb_button et_pb_bg_layout_dark et_pb_module et_flex_module preset--module--divi-button--default\" href=\"https:\/\/arsacs.com\/fr\/persons-with-arsacs\/\">Pour en savoir plus<\/a><\/div><\/div>\r\n\r\n<div class=\"et_pb_column_5 et_pb_column et_flex_column et_pb_css_mix_blend_mode_passthrough et_clickable et_flex_column_8_24 et_flex_column_8_24_tablet et_flex_column_24_24_phone\">\r\n\r\n<div class=\"et_pb_image_2 et_pb_image et_pb_module et_flex_module\"><span class=\"et_pb_image_wrap\"><img loading=\"lazy\" decoding=\"async\" src=\"https:\/\/arsacs.com\/wp-content\/uploads\/2026\/05\/Research-blurb.jpg\" title=\"R\u00e9sum\u00e9 de recherche\" width=\"1500\" height=\"1000\" srcset=\"https:\/\/arsacs.com\/wp-content\/uploads\/2026\/05\/Research-blurb.jpg 1500w, https:\/\/arsacs.com\/wp-content\/uploads\/2026\/05\/Research-blurb-1280x853.jpg 1280w, https:\/\/arsacs.com\/wp-content\/uploads\/2026\/05\/Research-blurb-980x653.jpg 980w, https:\/\/arsacs.com\/wp-content\/uploads\/2026\/05\/Research-blurb-480x320.jpg 480w\" sizes=\"(min-width: 0px) and (max-width: 480px) 480px, (min-width: 481px) and (max-width: 980px) 980px, (min-width: 981px) and (max-width: 1280px) 1280px, (min-width: 1281px) 1500px, 100vw\" class=\"wp-image-26320\" \/><\/span><\/div>\r\n\r\n<div class=\"et_pb_icon_1 et_pb_icon et_pb_module et_flex_module\"><span class=\"et_pb_icon_wrap\"><span class=\"et-pb-icon\">\uf492<\/span><\/span><\/div>\r\n\r\n<div class=\"et_pb_text_3 et_pb_text et_pb_bg_layout_light et_pb_module et_flex_module\"><div class=\"et_pb_text_inner\"><h3>Chercheurs<\/h3>\n<p>La Fondation soutient les chercheurs de l\u2019ARSACS en finan\u00e7ant les projets, fournissant des outils de recherche et en participant\/organisant des conf\u00e9rences. De plus, la Fondation  est \u00e0 la recherche de partenaires pour la r\u00e9alisation d\u2019essais pr\u00e9cliniques et cliniques.<\/p>\n<\/div><\/div>\r\n\r\n<div class=\"et_pb_module et_pb_button_module_wrapper et_pb_button_2_wrapper preset--module--divi-button--default_wrapper\"><a class=\"et_pb_button_2 et_pb_button et_pb_bg_layout_dark et_pb_module et_flex_module preset--module--divi-button--default\" href=\"https:\/\/arsacs.com\/fr\/research\/\">Pour en savoir plus<\/a><\/div><\/div>\r\n\r\n<div class=\"et_pb_column_6 et_pb_column et-last-child et_flex_column et_pb_css_mix_blend_mode_passthrough et_clickable et_flex_column_8_24 et_flex_column_8_24_tablet et_flex_column_24_24_phone\">\r\n\r\n<div class=\"et_pb_image_3 et_pb_image et_pb_module et_flex_module\"><span class=\"et_pb_image_wrap\"><img loading=\"lazy\" decoding=\"async\" src=\"https:\/\/arsacs.com\/wp-content\/uploads\/2026\/03\/arsacs-community.jpg\" title=\"communaut\u00e9 arsacs\" width=\"800\" height=\"533\" srcset=\"https:\/\/arsacs.com\/wp-content\/uploads\/2026\/03\/arsacs-community.jpg 800w, https:\/\/arsacs.com\/wp-content\/uploads\/2026\/03\/arsacs-community-480x320.jpg 480w\" sizes=\"(min-width: 0px) and (max-width: 480px) 480px, (min-width: 481px) 800px, 100vw\" class=\"wp-image-25356\" \/><\/span><\/div>\r\n\r\n<div class=\"et_pb_icon_2 et_pb_icon et_pb_module et_flex_module\"><span class=\"et_pb_icon_wrap\"><span class=\"et-pb-icon\">\uf57d<\/span><\/span><\/div>\r\n\r\n<div class=\"et_pb_text_4 et_pb_text et_pb_bg_layout_light et_pb_module et_flex_module\"><div class=\"et_pb_text_inner\"><h3>Communaut\u00e9<\/h3>\n<p>La Fondation repose uniquement sur la g\u00e9n\u00e9rosit\u00e9 de donateurs priv\u00e9s et l\u2019aide de b\u00e9n\u00e9voles. Nous avons besoin de votre soutien pour poursuivre la mission.\n D\u00e9couvrez comment vous pouvez faire une diff\u00e9rence !<\/p>\n<\/div><\/div>\r\n\r\n<div class=\"et_pb_module et_pb_button_module_wrapper et_pb_button_3_wrapper preset--module--divi-button--default_wrapper\"><a class=\"et_pb_button_3 et_pb_button et_pb_bg_layout_dark et_pb_module et_flex_module preset--module--divi-button--default\" href=\"https:\/\/arsacs.com\/fr\/fundraising\/\">Pour en savoir plus<\/a><\/div><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"","protected":false},"author":6,"featured_media":14625,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-12240","page","type-page","status-publish","has-post-thumbnail","hentry"],"_links":{"self":[{"href":"https:\/\/arsacs.com\/fr\/wp-json\/wp\/v2\/pages\/12240","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/arsacs.com\/fr\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/arsacs.com\/fr\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/arsacs.com\/fr\/wp-json\/wp\/v2\/users\/6"}],"replies":[{"embeddable":true,"href":"https:\/\/arsacs.com\/fr\/wp-json\/wp\/v2\/comments?post=12240"}],"version-history":[{"count":88,"href":"https:\/\/arsacs.com\/fr\/wp-json\/wp\/v2\/pages\/12240\/revisions"}],"predecessor-version":[{"id":26772,"href":"https:\/\/arsacs.com\/fr\/wp-json\/wp\/v2\/pages\/12240\/revisions\/26772"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/arsacs.com\/fr\/wp-json\/wp\/v2\/media\/14625"}],"wp:attachment":[{"href":"https:\/\/arsacs.com\/fr\/wp-json\/wp\/v2\/media?parent=12240"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}