{"id":22784,"date":"2025-09-25T14:29:23","date_gmt":"2025-09-25T18:29:23","guid":{"rendered":"https:\/\/www.arsacs.com\/?p=22784"},"modified":"2025-09-28T14:07:04","modified_gmt":"2025-09-28T18:07:04","slug":"advanced-mri-studies-to-achieve-microstructural-insight-and-identifyimaging-biomarkers-in-arsacs-dre-roberta-la-piana","status":"publish","type":"post","link":"https:\/\/arsacs.com\/fr\/advanced-mri-studies-to-achieve-microstructural-insight-and-identifyimaging-biomarkers-in-arsacs-dre-roberta-la-piana\/","title":{"rendered":"&#8220;Advanced MRI studies to achieve microstructural insight and identifyimaging biomarkers in ARSACS &#8221; &#8211; Dre Roberta La Piana"},"content":{"rendered":"<p class=\"x_MsoNormal\"><span data-olk-copy-source=\"MessageBody\">The involvement of the corticospinal tracts (CST) and cerebellum are the disease hallmarks of ARSACS. Previous radiological studies documented the presence of specific findings which were described as\u00a0<b>linear hypointensities in T2-weighted images at the level of the pons<\/b>. <\/span>This finding has become very suggestive of ARSACS when seen in brain MRIs; however, its significance is still unclear, with some studies proposing that it could be due to abnormal developmental of the brain. We aim to use\u00a0<b>advanced Magnetic Resonance (MR) techniques<\/b>\u00a0that combine diffusion and magnetization transfer imaging to\u00a0<b>clarify the properties of the corticospinal tract<\/b> in individuals with ARSACS and thus clarify the meaning of the pontine findings. Additionally, we aim to\u00a0<b>confirm<\/b>\u00a0the presence of similar findings in the\u00a0<b><i>SACS<\/i>-mutant mouse model<\/b>, to verify its usefulness as a\u00a0<b>pre-clinical model<\/b>\u00a0for future therapeutic options.\u00a0<\/p>\n<p class=\"PANormalLevelIA\" style=\"text-align: justify;\">Financement : 95 420$<\/p>\n<p><strong>Ce projet a \u00e9t\u00e9 financ\u00e9 conjointement avec le Richardson Trust Fund qui a contribu\u00e9 50 000$\u00a0 \u00e0 ce projet.\u00a0<\/strong><\/p>\n<p>Dur\u00e9e: Un an<\/p>\n\n\n<div class=\"wp-block-media-text is-stacked-on-mobile\" style=\"grid-template-columns:19% auto\"><figure class=\"wp-block-media-text__media\"><img loading=\"lazy\" decoding=\"async\" width=\"683\" height=\"1024\" src=\"https:\/\/arsacs.com\/wp-content\/uploads\/2025\/09\/Roberta-La-Piana-28-683x1024.jpg\" alt=\"\" class=\"wp-image-22639 size-full\" srcset=\"https:\/\/arsacs.com\/wp-content\/uploads\/2025\/09\/Roberta-La-Piana-28-683x1024.jpg 683w, https:\/\/arsacs.com\/wp-content\/uploads\/2025\/09\/Roberta-La-Piana-28-200x300.jpg 200w, https:\/\/arsacs.com\/wp-content\/uploads\/2025\/09\/Roberta-La-Piana-28-768x1151.jpg 768w, https:\/\/arsacs.com\/wp-content\/uploads\/2025\/09\/Roberta-La-Piana-28-scaled.jpg 924w, https:\/\/arsacs.com\/wp-content\/uploads\/2025\/09\/Roberta-La-Piana-28-480x719.jpg 480w\" sizes=\"(max-width: 683px) 100vw, 683px\" \/><\/figure><div class=\"wp-block-media-text__content\">\n<p>Dre Roberta La Piana<br>Institut Neurologique de Montr\u00e9al<br>3801 rue University<br>H3A 2B4 Montreal, QC<\/p>\n\n\n\n<p>Coordonn\u00e9es:&nbsp;<a href=\"mailto:roberta.lapiana@mcgill.ca\">roberta.lapiana@mcgill.ca<\/a><\/p>\n<\/div><\/div>\n","protected":false},"excerpt":{"rendered":"<p>The involvement of the corticospinal tracts (CST) and cerebellum are the disease hallmarks of ARSACS. Previous radiological studies documented the presence of specific findings which were described as\u00a0linear hypointensities in T2-weighted images at the level of the pons. This finding has become very suggestive of ARSACS when seen in brain MRIs; however, its significance is [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_et_pb_use_builder":"","_et_pb_old_content":"","_et_gb_content_width":"","inline_featured_image":false,"footnotes":""},"categories":[35],"tags":[],"class_list":["post-22784","post","type-post","status-publish","format-standard","hentry","category-projets-de-recherche"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>&quot;Advanced MRI studies to achieve microstructural insight and identifyimaging biomarkers in ARSACS &quot; - Dre Roberta La Piana - ARSACS<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/arsacs.com\/fr\/advanced-mri-studies-to-achieve-microstructural-insight-and-identifyimaging-biomarkers-in-arsacs-dre-roberta-la-piana\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"&quot;Advanced MRI studies to achieve microstructural insight and identifyimaging biomarkers in ARSACS &quot; - Dre Roberta La Piana - ARSACS\" \/>\n<meta property=\"og:description\" content=\"The involvement of the corticospinal tracts (CST) and cerebellum are the disease hallmarks of ARSACS. Previous radiological studies documented the presence of specific findings which were described as\u00a0linear hypointensities in T2-weighted images at the level of the pons. This finding has become very suggestive of ARSACS when seen in brain MRIs; however, its significance is [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/arsacs.com\/fr\/advanced-mri-studies-to-achieve-microstructural-insight-and-identifyimaging-biomarkers-in-arsacs-dre-roberta-la-piana\/\" \/>\n<meta property=\"og:site_name\" content=\"ARSACS\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/profile.php?id=100044457429916\" \/>\n<meta property=\"article:published_time\" content=\"2025-09-25T18:29:23+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2025-09-28T18:07:04+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/arsacs.com\/wp-content\/uploads\/2025\/09\/Roberta-La-Piana-28-scaled.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"924\" \/>\n\t<meta property=\"og:image:height\" content=\"1384\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"ARSACS\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Written by\" \/>\n\t<meta name=\"twitter:data1\" content=\"ARSACS\" \/>\n\t<meta name=\"twitter:label2\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data2\" content=\"1 minute\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\\\/\\\/arsacs.com\\\/fr\\\/advanced-mri-studies-to-achieve-microstructural-insight-and-identifyimaging-biomarkers-in-arsacs-dre-roberta-la-piana\\\/#article\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/arsacs.com\\\/fr\\\/advanced-mri-studies-to-achieve-microstructural-insight-and-identifyimaging-biomarkers-in-arsacs-dre-roberta-la-piana\\\/\"},\"author\":{\"name\":\"ARSACS\",\"@id\":\"https:\\\/\\\/arsacs.com\\\/#\\\/schema\\\/person\\\/93b66d6b897bfa131622d04b767b15f1\"},\"headline\":\"&#8220;Advanced MRI studies to achieve microstructural insight and identifyimaging biomarkers in ARSACS &#8221; 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